Perivascular malignant epithelioid cell tumor (PEComa) of the uterus:
نویسندگان
چکیده
Perivascular epithelioid cell tumors, called PEComas, have a mesenchymal origin with immunoreactivity for melanocytic and smooth muscle markers. Its incidence in the form of uterine involvement is rare, between 1 2 cases per million inhabitants, affecting mainly women their fifth decade life. The present study was elaborated according to rules CARE case report. patient's medical record analyzed, who authorized access it signed Free Informed Consent Form, together those involved this work. This patient underwent treatment follow-up supervisor Therefore, aimed describe rare clinical report malignant perivascular tumor (PEComa). Although literature on subject scarce there are no consistent criteria diagnosis treatment, our question presented aspects unfavorable evolution (a large number cytological atypia high mitotic index) characterizing PEComa uncertain potential, requiring adjuvant after surgery. evolved well surgery undergoing quarterly follow-ups at oncology gynecology outpatient clinic, physical examination nuclear magnetic resonance pelvis control purposes.
منابع مشابه
Malignant perivascular epithelioid cell tumor of the uterus
Perivascular epithelioid cell tumors (PEComas) are a rare collection of tumors arising in a wide array of anatomic locations and characterized by a myomelanocytic phenotype. PEComas which occur in non-classic anatomic distributions are known as perivascular epithelioid cell tumor-not otherwise specified (PEComa-NOS), and one of the most common primary sites for PEComa-NOS is the uterus. The ris...
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Perivascular epithelioid cell tumors (PEComas) are mesenchymal tumors composed of histologically, immunohistochemically, ultrastructurally, and genetically distinctive cells. PEComas have been described in different organs and are considered ubiquitous tumors. In this review we discuss recent informations related to PEComas in the genitourinary tract.
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INTRODUCTION Perivascular epithelioid cell tumor (PEComa) is a mesenchymal neoplasm composed of perivascular epithelioid cells with clear to eosinophilic cytoplasm. Pigmented PEComa arising from kidney is extraordinarily rare and sometimes can exhibit aggressive biological behavior. CASE REPORT We present here a rare case of pigmented renal PEComa in a 46-year-old female. The patient had comp...
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PEComas are uncommon mesenchymal tumors often involving the pelvic organs. They have an unpredictable behavior. Accurate diagnosis and long-term follow-up is therefore essential in these patients. We report this case of PEComa of uncertain malignant potential in an unusual location with excellent prognosis.
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ژورنال
عنوان ژورنال: MedNEXT Journal of Medical and Health Sciences
سال: 2023
ISSN: ['2763-5678']
DOI: https://doi.org/10.54448/mdnt23201